Request PDF on ResearchGate | Síndrome de aglutininas frías y púrpura trombocitopénica autoinmune: Un caso inusual de síndrome de. Abstract. ARANGO, Marcos; ARENAS, Mario and MARTINEZ, Octavio. Mycoplasma pneumoniae pneumonia complicated by cold agglutinin hemolytic anemia. QUINTANILLA-GALLO, Júvel; MARCHENA- PICADO, Margarita and GOURZONG- TAYLOR, Charles. Síndrome aglutininas frías. Acta méd. costarric [ online].
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Health care resources for this disease Expert centres Diagnostic tests 0 Patient organisations 4 Orphan drug s 0.
Orphanet: Doenca de aglutininas frias
If you are using a modern web browser, you may instead navigate to the newer desktop version of fpnotebook. It occurs more frequently after the age of A cold environment or a concurrent infection may trigger or exacerbate the condition, and episodes of acute hemolysis with hemoglobinemia and hemoglobinuria are more common in winter.
Definition NCI An acquired anemia caused by destruction of the red blood cells by autoantibodies. In secondary cases, lymphocytosis, with the presence of atypical lymphocytes on the smear, can be found in peripheral blood. An acquired anemia caused by destruction of the red blood cells by autoantibodies.
Examination Chapter related topics Plasmic Score. Differential diagnosis The differential diagnosis for cold agglutinin disease is mixed AIHA see this term. Diagnostic methods In some cases, the diagnosis is made by chance on a standard complete blood count CBC detecting abnormal agglutination of the red blood cells. The documents contained in this web site are presented for information purposes only. Anemia emolitica da emoagglutinine fredde, Malattia da agglutinina fredda, Malattia da agglutinine a frigore, Malattia da agglutinine fredda.
In the presence of underlying lymphoma, chlorambucil or oral cyclophosphamide may be helpful.
Although access to this page is not restricted, the information found here aglutininsa intended for aglutinina by medical providers. Clinical description It occurs more frequently after the age of Cold agglutinin disease manifests as acute or chronic hemolytic anemia, with associated pallor and fatigue. A condition in which the body’s immune system stops red blood cells from forming or causes them to clump together.
Management and treatment Patients with few clinical symptoms and mild anemia may not require treatment but only avoidance of cold.
Keeping the patient warm may be sufficient treatment. The disease may appear abruptly with anemia and hemoglobinuria, or onset may be more gradual and insidious. You are currently viewing the original ‘fpnotebook.
Neumonia por Mycoplasma pneumoniae complicada con anemia hemolitica por aglutininas frias.
Patients with few clinical symptoms and mild anemia may not require treatment but only avoidance of cold. In some cases, the diagnosis is made by chance on a standard complete blood count CBC detecting abnormal agglutination of the red blood cells. Specialised Social Services Eurordis directory.
Rituximab may be an option for treatment in some cases. For all other comments, please send your remarks via contact us. Immune complex alutininas anemia can occur in patients who have chronic lymphocytic leukemia CLL.
Please Contact Me as you run across problems with any of these versions on the website. Only comments written in English can be processed. Prognosis The disease has a chronic course and the outcome is usually benign, except in patients with recurrent episodes of severe anemia or in frais the underlying B-cell lymphoma has an aggressive course.
Idiopathic and lymphoma-associated cold AIHA tend to be chronic while infections tend to cause an acute disease. Summary and related texts. Causes include autoimmune disorders, lymphoproliferative disorders, and infections. Autoimmune hemolytic anemia can occur in patients who have chronic lymphocytic leukemia CLL.
Etiology Cold agglutinin disease can be primary idiopathic or secondary, caused by an underlying condition, such as infection Mycoplasma pneumoniaelymphoproliferative disorders, systemic autoimmunity or neoplasm. Definition CSP due to acquired antierythrocyte autoantibodies causing premature erythrocyte clearance by the spleen; antibodies can be warm or cold active; usually slow developing and treatable.
The disease has a chronic course and the outcome is usually benign, except in patients with recurrent episodes of severe anemia or in whom the underlying B-cell lymphoma has an aggressive course. Check this box if you wish to receive a copy of your message.